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Syringocystadenoma papilliferum with sebaceous differentiation in an
intradermal tubular apocrine component. Report of a case.
Am J Dermatopathol. 2008 Feb;30(1):51-3.
Syringocystadenoma papilliferum is a benign tumor most commonly
located on the scalp or face, and it often arises within a nevus
sebaceus of Jadassohn. We describe a 61-year-old man with
syringocystadenoma papilliferum developing within a nevus sebaceus
with sebaceous differentiation in an intradermal tubular apocrine
component of the syringocystadenoma papilliferum. Although some
adnexal neoplasms that develop in association with a nevus sebaceus
may exhibit conjoint sebaceous, follicular, or apocrine
differentiation, reflecting close embryological relations of the
folliculosebaceous-apocrine unit, the feature we report on has not
previously been described to the best of our knowledge.
Syringocystadenocarcinoma papilliferum: successfully treated with Mohs
micrographic surgery.Dermatol
Surg. 2004 Mar;30(3):468-71.
BACKGROUND:
Syringocystadenocarcinoma papilliferum, a rare sweat gland carcinoma,
is the malignant counterpart of syringocystadenoma papilliferum.
OBJECTIVE: To demonstrate a rare case of syringocystadenocarcinoma
papilliferum successfully treated with Mohs micrographic surgery.
METHODS: A 60-year-old male presented with two verrucous plaques on
his right auricle since childhood. These two plaques became ulcerated,
more painful, and pruritic in 1 year. Histopathologic examination
revealed syringocystadenocarcinoma papilliferum. RESULTS: Mohs
micrographic surgery with reconstruction of right auricle was
performed subsequently. There are no signs of recurrence or metastasis
6 years after operation. CONCLUSION: Syringocystadenocarcinoma
papilliferum can be successfully treated with Mohs micrographic
surgery. |
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Syringocystadenoma
Papilliferum
Visit:
Dermpath-India
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Syringocystadenoma papilliferum: a rare breast tumor in a young boy.Pediatr
Dev Pathol. 2006 Sep-Oct;9(5):381-3.
Syringocystadenoma papilliferum of the breast is extremely rare in
children. However, some occasional cases have been diagnosed in
females. This report documents a case of syringocystadenoma
papilliferum occurring in a healthy 4-year-old male.
Histopathologically, this tumor, located deep in the dermis, was
characterized by the presence of papillary projections extending
into the lumen of epithelial cystic invaginations in a background of
dense fibrous tissue. The papillary projections and the duct-like
structures were lined by an inner columnar epithelium, which
demonstrated luminal apical decapitation secretion, and had an outer
layer of smaller cuboidal cells. These findings support apocrine
differentiation in this case. A fairly dense mononuclear infiltrate
in the stroma of the tumor, especially in the papillary projections,
was also present. Although syringocystadenoma papilliferum is rare
in children, it should not be summarily ruled out during
examinations of masses found in the pediatric male breast. It is
important to recognize this unusual location of the tumor so that a
prompt diagnosis, based on histopathology and surgical excision, can
be proposed. |
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March 2008
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