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Desmoplastic small round cell tumor masquerading as advanced ovarian
cancer. Int
J Gynecol Cancer. 2007 Dec 14.
Desmoplastic
small round cell tumor (DSRCT) is a rare abdominal malignancy usually
diagnosed in young adult males. Most patients have widespread disease
at presentation, with an organ of origin difficult to ascertain. A
33-year-old female presented to her gynecologist with complaints of
suprapubic pressure, abdominal pain, and increased abdominal girth.
She had a large intraabdominal tumor on ultrasound, thought to be
ovarian cancer. She underwent surgical exploration, which confirmed a
malignancy, but the exact etiology was uncertain. Final pathology was
consistent with DSRCT. DSRCT is a rare malignancy that can mimic other
more commonly seen tumors such as lymphoma and ovarian cancer. When
encountering an extensive intraabdominal malignancy of uncertain
etiology, DSRCT should be in the differential diagnosis. |